|
KMID : 1035220210130020059
|
|
Korean Journal of Neuromuscular Disorders
2021 Volume.13 No. 2 p.59 ~ p.63
|
|
|
A Case of POEMS Syndrome Previously Diagnosed with Extramedullary Plasmacytoma
|
|
Kim Hyun-Kee
Lee Sang-Gon
|
|
|
Abstract
|
|
|
|
POEMS (polyneuropathy, organomegaly, endocrinopathy, monoclonal gammopathy and skin changes) syndrome is a rare multisystem disorder associated with osteosclerotic myeloma. It is characterized by peripheral polyneuropathy, presence of monoclonal plasma cell proliferative disorder, and one or more of the following features - sclerotic bone lesions, Castleman disease, elevated levels of vascular endothelial growth factor, organomegaly, extravascular volume overload, endocrinopathy, skin changes, papilledema, and thrombocytosis. Extramedullary plasmacytoma (EMP) is a rare plasma cell neoplasm that arises in isolated tissues without bone marrow involvement or systemic characteristics of multiple myeloma. Herein, we report a male patient who was previously diagnosed with EMP and later developed POEMS.
|
|
|
KEYWORD
|
|
|
POEMS syndrome, Extramedullary plasmacytoma, Monoclonal gammopathy
|
|
|
FullTexts / Linksout information
|
|
|
|
|
|
Listed journal information
|
|
|
|
|